Angiosarcoma of the caecum

Introduction. Primary angiosarcomas arising from the digestive system are rare, representing less than 1% percent of malignant sarcomas. Only a few cases have been reported in literature. Colorectal involvement is exceedingly uncommon and harbinger poor prognosis with widespread metastasis. Diagnosis often delayed due to non-specific symptoms pathology which mimics other tumors. Case outline. A 52-year-old woman was presented emergency room July 2021, complaining protracted malaise, rapid fatigue occasional sweating. Multislice computed tomography (MSCT) abdomen small pelvis revealed existence lobular, well vascularized, supravesical lesion, located along anterior contour uterine corpus, convolutes intestine. The patient subjected operative treatment curative intent. Intraoperatively, completely tumor-altered caecum verified Standard histopathological examination demonstrated high grade epithelioid angiosarcoma severe pleomorphism solid growth pattern. control MSCT done 12 months after operation did not show any pathological lesions. Conclusion. Both clinical diagnoses colorectal challenging. Patients presenting symptoms, can lead mismanagement late diagnosis. diagnosis relies on immunohistochemical staining for endothelial markers. In limited tissue biopsies, it be easily misdiagnosed as poorly differentiated adenocarcinoma or gastrointestinal stromal tumor. For now, surgical R0 resection seems only effective modality.